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- Budesonide
- Dextromethorphan and Qunidine
- Mafenide
- AGA : aspartylglucosaminidase
- SLC12A1 : solute carrier family 12 member 1
- BCS1L : BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone
- GAMT : guanidinoacetate N-methyltransferase
- UGT1A1 : UDP glucuronosyltransferase family 1 member A1
- GATM : glycine amidinotransferase
- NAGA : alpha-N-acetylgalactosaminidase
- IDUA
- NAGLU : N-acetyl-alpha-glucosaminidase
- HGSNAT : heparan-alpha-glucosaminide N-acetyltransferase
- HYAL1
- GUSB : glucuronidase beta
- NEU1 : neuraminidase 1
- PCCB : propionyl-CoA carboxylase subunit beta
- HEXB
- NANS
- ACPT