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- ACY1 : aminoacylase 1
- CYP19A1 : cytochrome P450 family 19 subfamily A member 1
- ASNS : asparagine synthetase (glutamine-hydrolyzing)
- CPS1 : carbamoyl-phosphate synthase 1
- IARS2
- AARS1 alanyl-tRNA synthetase 1
- ASS1 : argininosuccinate synthase 1
- ACSF3 : acyl-CoA synthetase family member 3
- EARS2 : glutamyl-tRNA synthetase 2, mitochondrial
- FARS2
- TARS2
- ALDH18A1 : aldehyde dehydrogenase 18 family member A1
- KARS1
- GCLC
- GLUL
- GSS : glutathione synthetase
- GNMT : glycine N-methyltransferase
- IARS1
- HLCS : holocarboxylase synthetase
- HMBS : hydroxymethylbilane synthase